|
Neuromuscular Scoliosis
The term
"neuromuscular scoliosis" is used to describe curvature
of the spine in children with any disorder of the
neurological system. Common categories include cerebral
palsy, spina bifida, muscular dystrophies, spinal cord
injuries and so forth. Most of these children have as a
unifying feature weakness of the trunk. As they grow and
their trunk gets weaker, there is a progressive,
collapsing deformity of the spine producing a long,
c-type curve. These curves tend to be progressive, with
the rate of progression becoming worse during rapid
growth. For children confined to a wheel chair,
progressive curves may affect the child's ability to be
seated comfortably, thereby affecting their quality of
life and function.

The treatment of
neuromuscular scoliosis must be individualized. Bracing
may provide support for the trunk in the seated
position, but is usually not effective at stopping
progression of the curve over time. Seating
modifications such as inserts into wheelchairs may help
with positioning the child, but are also not corrective
in terms of the scoliosis. Alternative therapies such as
insertion of an Intrathecal Baclophen Pump will produce
a reduction in spasticity but will not affect the
long-term progression of the scoliosis. Injection of
Botox into the paraspinal musculature will temporarily
reduce the tone in these muscles but has no proven
long-term efficacy in the treatment of neuromuscular
curves.
The fundamental
question to be addressed by families and their treating
doctor is whether the preservation of the ability to sit
by invasive surgery will maintain or improve the child's
quality of life and function. For some children with
cognitive or visual/sensory impairment, these decisions
are difficult. Parents often struggle with the fact that
they are unable to explain to the child why they are
having surgery and help them understand that pain
accompanying the procedure. These can be difficult
questions to answer given the risks, costs, and recovery
associated with this type of surgery. These decisions
should be made with great care. Talking with other
families who have been through this decision process is
very helpful. Ultimately, parents will have to make this
difficult decision for their child.
|